Aspectos multidisciplinares e manifestações clínicas secundárias sa sequência de Pierre Robin:Uma revisão integrativa
Keywords:
Fenda Labial, Fissura Palatina, Síndrome de Pierre Robin.Abstract
Introdução: A Sequência de Pierre Robin (SPR) é caracterizada por micrognatia, glossoptose, e presença de fissura palatina. Como consequências desta alteração são notados clinicamente comprometimento respiratório e dificuldade alimentar. No entanto, os sinais clínicos secundários relacionados a esta doença, bem como, a relevância do atendimento multidisciplinar e da capacitação dos cuidadores raramente são discutidos na literatura. Objetivo: Realizar uma revisão integrativa acerca das manifestações clínicas secundárias e dos aspectos multidisciplinares relacionados à SPR. Materiais e Métodos: Foi realizada uma revisão integrativa, através de uma busca computadorizada utilizando os descritores “Cleft Lip” AND/OR “Cleft Palate” AND “Pierre Robin Syndrome” em bases de dados de literatura científica, seguindo critérios metodológicos pré-estabelecidos. Os estudos selecionados foram analisados na íntegra, tabulados e discutidos de maneira descritiva. Resultados: Após o levantamento bibliográfico, 28 artigos responderam o propósito desta revisão. Os aspectos multidisciplinares relacionados à SPR incluíram os seguintes tópicos: diagnóstico, etiopatogenia da doença, taxa de mortalidade dos pacientes, avaliação dimensional da fissura e importância da promoção do autocuidado. As manifestações clínicas secundárias da doença compreenderam anomalias dentárias e alterações ósseas, musculares e cardíacas. Conclusão: A SPR apresenta diagnóstico e etiopatogenia complexos, e os portadores dessa condição apresentam maior risco de mortalidade em decorrência do grave comprometimento respiratório e risco de desnutrição. As manifestações clínicas secundárias podem ocorrer por danos locais ou sistêmicos, e caracterizar um fator isolado ou compor uma condição sindrômica.Downloads
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